The adipose tissue metabolism of patients suffering from Von Gierke disease resembles the adipose tissue metabolism of a individual. A) Healthy

B) Starved

The correct option is B

Explanation:

Von Gierke disease is an inborn error of metabolism (hereditary disorder) in which the body cannot convert glycogen (storage form of glucose in liver and muscle) back to glucose. This disorder is caused by the deficiency of the enzymes glucose-6-phosphatase or glucose-6-phosphate translocase. This generally causes blood sugar to be low (since liver releases this excess sugar to the body in the form of glycogenolysis when the body needs it).

Since the body cannot derive energy from the glucose present in the liver and muscle, the adipose tissue which is a storage site for energy in the form of fat is usually depleted as it becomes the alternative path for energy production (for some organs) just as in a starved individual who has had his/her glycogen storage depleted.